Pehea eʻai ai i ka PKU Diet

Pono kaʻai PKU no ka poʻe i loaʻa ka maʻiʻeha i kapaʻia he phenylketonuria (PKU). Loaʻa nā kānaka me phenylketonuria i kahi enzyme e hiki ai i ke kino ke hoʻololi i phenylalanine (amino acid) i tyrosine (kekahi amino acid ). Ke kūkulu nei ka phenylalanine a hoʻoweliweli i ka lolo; no laila, pono i nā mea a pau me PKU keʻalo i nā meaʻai momona.

Pono nā'ōpiopio a me nā keiki me PKU i kahiʻano kūikawāʻaʻole i loko o phenylalanine.

He mea koʻikoʻi loaʻaʻoleʻai nā keiki, nā kamaliʻi, a me nā keiki i nā meaʻai waiwaiʻona pilikino no ka uluʻana o ka lolo. Pono e mālamaʻia kekahiʻai maʻamau. Pono e hōʻoleʻia nā meaʻai a pau i kiʻekiʻe i ka protein.

Piʻi nā meaʻai i loko o ka pilina:

ʻO nā pāʻina, nā'āpala, a me nā meaʻai e hanaʻia me kēia mau meaʻai, pono e hōʻoleʻia - pēlā pizza, keke, nā kuki, nā hamburgers, nā'īlio wela, ka ice cream, ka yogurt a me nā meaʻai'ē aʻe. ʻO nā mea e like me ka berena a me kekahiʻano o ka meaʻai e hiki ke loaʻa i ka waiwai nui. Pono eʻaeʻiaʻo Aspartame ma muli o ka huiʻana o ka wai aspartic a me phenylalanine.

Hiki i nā keiki a me nā'ōpio me PKU keʻai i nā hua a me nā huaʻai a me nā liʻiliʻi o nā meaʻai a me nā mea paʻakikī no ka meaʻaʻole i liʻiliʻi ia mau meaʻai i loko o ka meaola. Pono pono nā mākua e pili pono i kaʻai.

Akā,ʻo ka meaʻoi aku ka PKU ma lalo o ka pilina no ke olakino maikaʻi, no lailaʻo nā keiki a me nā mākua me ka PKU pono eʻai i nā meaola maloʻo kūikawā i hanaʻia me ka phenylalanine.

Eia kekahi, pono e mālamaʻia kēiaʻai no ke ola, a ke lawe pinepineʻia nei nā ho'āʻo koko e mālama i keʻano o nā phenylalanine i loko o ke kino.

ʻO ka PKU maʻamau?

Wahi a ka National PKU Alliance, e pili ana i kahi i 15,000 mau keiki he PKU. ʻO nā keiki maʻAmelika Huipūʻia a me nā'āina'ē he nui ke nānāʻia ma hope koke iho o ka hānauʻana, a no ka mālamaʻana o nā pēpē a me nā keiki i ka meaʻai, e ulu ana ko lākou naʻau i keʻano.

Hiki i nā mākua a me ka PKU ke hoʻonui iki i ke komoʻana o ka pilikino ma muli o ka hoʻomohalaʻana o ka lolo, akāʻaʻole hiki i ka PKU ke hele aku a lilo i ka nui o phenylalanine e hiki ke hoʻopilikia i nā pilikia o ka naʻau a me ka nalowale o kaʻike.

Nā kumuhana:

LIKE LIKE LIKE "Ka Mea'Āina MeaʻAi Loa." Ke Kumukūmāhiku o ka Buke, Nūpepa NJ, USA: Wiley-Blackwell Publishing,ʻOkakopa 2011.

Merck Manual - Kauoha. "'Amino Acid a me Organic Acid Mīkini Holopili." http://www.merckmanuals.com/professional/pediatrics/inherited-disorders-of-metabolism/overview-of-amino-acid-and-organic-acid-metabolism-disorders.

ʻO National Phenylketonuria Alliance. "Nā Phenylketonia Pono no ke Kula a me nā Kauoha." http://www.npkua.org/Portals/0/PKU_schoolfacts.pdf .